Isolated Large Vessel Pulmonary Vasculitis as a Cause of Chronic Obstruction of the Pulmonary Arteries

PVRI Member Authors: Colin Church, Joanna Pepke-Zaba


Isolated pulmonary artery involvement by large vessel vasculitis is rare. This case report describes two patients with large vessel pulmonary vasculitis initially thought to have chronic thromboembolic pulmonary hypertension who had their diagnosis revised following pulmonary endarterectomy surgery. Advances in imaging techniques such as positron emission tomography and magnetic resonance imaging have permitted complementary radiological methods of diagnosis and follow up of large vessel disease and these are discussed in conjunction with the immunosuppressive and operative management of these patients.

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Pathology and Pathophysiology


Guy Hagan, Deepa Gopalan, Colin Church, Doris Rassl, Chetan Mukhtyar, Trevor Wistow, Chim Lang, Pasupathy Sivasothy, Susan Stewart, David Jayne, Karen Sheares, Steven Tsui, David P. Jenkins, Joanna Pepke-Zaba

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Pulmonary Circulation Vol 1: No 3 cover image

September 2011

Pulmonary Circulation Vol 1: No 3

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