The chest x-ray is abnormal in 90% of people with idiopathic pulmonary arterial hypertension (IPAH) at the time of diagnosis. Typical changes include enlarged pulmonary arteries with peripheral pruning of vessels and cardiomegaly. There may be changes suggesting an alternative cause of pulmonary hypertension such as lung disease or pulmonary venous congestion.
Links to further reading:
- Rich et al. Primary pulmonary hypertension. A national prospective study. Annals of Internal Medicine 1987; 107:216-223
- The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS). 2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. European Heart Journal (2016) 37, 67–119
- Sproule, M. Chapter 8. Imaging. In Pulmonary Circulation. Diseases and their Treatment Ed Peacock et al. 2016. 138-152
- Ryan JR et al. The WHO classification of pulmonary hypertension: A case-based imaging compendium. Pulmonary Circulation 2012; 2:107-121