Patients with pulmonary arterial hypertension (PAH) experience long diagnostic delays, high functional class at diagnosis and poor prognosis. We aimed to study the differentiative and predictive value of 90 inflammatory and immunomodulatory related proteins in idiopathic and hereditary PAH (IPAH/HPAH) and systemic sclerosis-associated PAH (SSc-APAH). 

Connective tissue disease-associated pulmonary arterial hypertension (CTD-PAH) has a poorer prognosis than idiopathic PAH, potentially attributable to pulmonary veno-occlusive disease (PVOD)-like involvement. 

Presented at PVRI 2026 Congress by Eric Austin, Vanderbilt University Medical Center

Presented at PVRI 2026 Congress by James Klinger, Alpert Medical School of Brown University

Presented at PVRI 2026 Congress by Jair Tenorio, Institute of Medical & Molecular Genetics (INGEMM), La Paz University Hospital

Presented at PVRI 2026 Congress by Vasile Foris, Medical University of Graz

Presented at PVRI 2026 Congress by Stephen Archer, Queen's University

Presented at PVRI 2026 Congress by Monica Mora, Institute of Medical & Molecular Genetics (INGEMM)

Presented at PVRI 2026 Congress by Natalia Gallego-Zazo, Instituto De Genética Médica Y Molecular

Presented at PVRI 2026 Congress by Richard Trembath, King's College London